Anti-GORAB Rabbit Polyclonal Antibody (Alexa Fluor® 488)

Lieferant: Bioss
BS-6643R-A488
BOSSBS-6643R-A488EA 893 EUR
BOSSBS-6643R-A488
Anti-GORAB Rabbit Polyclonal Antibody (Alexa Fluor® 488)
Antikörper
Defects in GORAB are the cause of geroderma osteodysplasticum (GO) [MIM:231070]; also known as gerodermia osteodysplastica or Walt Disney dwarfism. GO is a rare autosomal recessive disorder characterized by lax, wrinkled skin, joint laxity and a typical face with a prematurely aged appearance. Skeletal signs include severe osteoporosis leading to frequent fractures, malar and mandibular hypoplasia and a variable degree of growth retardation.

Recommended Dilutions: IF(IHC-P): 1:50-200

Type: Primary
Antigen: SCYL1BP1
Clonality: Polyclonal
Clone:
Conjugation: Alexa Fluor® 488
Epitope:
Host: Rabbit
Isotype: IgG
Reactivity: Human, Mouse, Rat
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