Anti-Dihydropyrimidinase Rabbit Polyclonal Antibody (Alexa Fluor® 680)

Lieferant: Bioss
BS-8287R-A680
BOSSBS-8287R-A680EA 893 EUR
BOSSBS-8287R-A680
Anti-Dihydropyrimidinase Rabbit Polyclonal Antibody (Alexa Fluor® 680)
Antikörper
Catalyzes the second step of the reductive pyrimidine degradation, the reversible hydrolytic ring opening of dihydropyrimidines. Can catalyzes the ring opening of 5,6-dihydrouracil to N-carbamyl-alanine and of 5,6-dihydrothymine to N-carbamyl-amino isobutyrate.Tissue specificity:Liver and kidney.Involvement in disease:Defects in DPYS are the cause of dihydropyrimidinase deficiency (DHPD). DHPD is an autosomal recessive disorder characterised by dihydropyrimidinuria and associated with a variable clinical phenotype: epileptic or convulsive attacks, dysmorphic features and severe developmental delay, and congenital microvillous atrophy.

Type: Primary
Antigen: Dihydropyrimidinase
Clonality: Polyclonal
Clone:
Conjugation: ALEXA FLUOR® 680
Public Immunogen Range: 121-220/519
Host: Rabbit
Isotype: IgG
Reactivity:
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